Contribution of the Unfolded Protein Response (UPR) to the Pathogenesis of Proteasome-Associated Autoinflammatory Syndromes (PRAAS)

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Contribution of the Unfolded Protein Response (UPR) to the Pathogenesis of Proteasome-Associated Autoinflammatory Syndromes (PRAAS). Poli MC, et al..pdf (1.05 MB)

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2019

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Article

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Artículos Medicina y Ciencias de la Salud

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Frontiers

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http://hdl.handle.net/11447/3179
 https://doi.org/10.3389/fimmu.2019.02756

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Abstract

Type I interferonopathies cover a phenotypically heterogeneous group of rare genetic diseases including the recently described proteasome-associated autoinflammatory syndromes (PRAAS). By definition, ...

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Citation

Ebstein F, Poli Harlowe MC, Studencka-Turski M and Krüger E (2019) Contribution of the Unfolded Protein Response (UPR) to the Pathogenesis of Proteasome-Associated Autoinflammatory Syndromes (PRAAS). Front. Immunol. 10:2756. doi: 10.3389/fimmu.2019.02756

Keywords

ER stress , TCF11/Nrf1 , Autoinflammation , mTORC1 , Proteasome , Unfolded protein response

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