A Case of Interstitial Lung Disease With Apical Pleural Thickening: Idiopathic Pleuroparenchymal Fibroelastosis

dc.contributor.authorLabarca, Gonzalo
dc.contributor.authorCabello, Hernán
dc.contributor.authorFernández‐Bussy, Sebastián
dc.contributor.authorCabello, Francisca
dc.contributor.authorDíaz, Juan
dc.date.accessioned2017-03-20T18:03:56Z
dc.date.available2017-03-20T18:03:56Z
dc.date.issued2014
dc.description.abstractIdiopathic pleuroparenchymal fibroelastosis (IPPFE) is a very rare, recently described condition, characterised by fibrotic thickening of the pleural and subpleural parenchyma, predominantly in the upper lobes.1 Clinical manifestations and lung function tests are similar to those observed in restrictive interstitial pneumonias, and in some of the cases described, there was a history of recurrent infections, such as allergic bronchopulmonary aspergillosis or cystic fibrosis.2,3 Radiological findings include intense pleural thickening associated with signs of fibrosis, particularly in the upper lobes, with loss of volume and structural distortion, as observed in the case presented here.
dc.format.extent2
dc.identifier.citationArch Bronconeumol 2014; Vol. 50 Num.1 p:48-49
dc.identifier.urihttp://hdl.handle.net/11447/1038
dc.identifier.urihttp://dx.doi.org/10.1016/j.arbr.2013.12.004
dc.language.isoen_US
dc.publisherSociedad Española de Neumología y Cirugia Torácica
dc.subjectInterstitial Lung Disease
dc.subjectApical Pleural Thickening
dc.subjectIdiopathic Pleuroparenchymal Fibroelastosis
dc.subjecteldery
dc.subjectfemale
dc.subjectLatin America
dc.titleA Case of Interstitial Lung Disease With Apical Pleural Thickening: Idiopathic Pleuroparenchymal Fibroelastosis
dc.typeArtículo

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